ECTODERMAL DYSPLASIA: CASE REPORT & LITERATURE REVIEW

Authors

  • Deepak passi , Gagan Mehta , kuldeep vishwakerma , pranshu singh Department of Oral and Maxillofacial Surgery, Faculty of Dental Sciences , King George’s Medical University, Lucknow , India

Keywords:

Ectodermal dysplasia’s, Christ-Siemens-Touraine syndrome, Clouston syndrome, onychodysplasias, O.P.G (ortho pentomo gram)

Abstract

Ectodermal dysplasia is an extremely rare hereditary disease characterized by a congenital dysplasia of one or more ectodermal structures and their accessory appendages. Common manifestations include defective hair follicles and eyebrows, frontal bossing with prominent supraorbital ridges, nasal bridge depression, and protuberant lips. Intraorally, common findings are anodontia or hypodontia, conical teeth, and, consequently, generalized spacing. The patient may suffer from dry skin, hyperthermia, and unexplained high fever as a result of the deficiency of sweat glands. The present review focuses on the clinical manifestations, classifications, and diagnosis of ectodermal dysplasia. Here we present a case report of a 22-year-old male, exhibited many of the manifestations of ectodermal dysplasia.

Downloads

Published

2013-11-01

How to Cite

pranshu singh, D. passi , G. M. , kuldeep vishwakerma , . (2013). ECTODERMAL DYSPLASIA: CASE REPORT & LITERATURE REVIEW. Indo-European Journal of Dental Therapy and Research, 1(3), 170–173. Retrieved from https://ijddmr.org/index.php/iejdtr/article/view/67

Issue

Vol. 1 No. 3 (2013)

Section

Articles